Artikel
Bobble-head-doll syndrome associated with suprasellar cyst in children: report of three cases
Das Bobble head doll Syndrom assoziert mit der suprasellären Zyste in Kindern: Beschreibung von drei Fällen
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Autoren
Veröffentlicht: | 4. Mai 2005 |
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Gliederung
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Objective
We report three cases of bobble-head-doll syndrome in children with suprasellar cysts who were treated with neuroendoscopic approach.
Methods
The history and clinical features of three children (two girls and a boy, 4,2 and 9 years old) with bobble-head-doll syndrome associated with suprasellar cyst are described.
The bobble-head-doll syndrome was the initial symptom in one case. In two other cases, the macrocephaly and psychomotor retardation were the first symptoms and the bobble head-doll syndrome developed later on. The obstructive hydrocephalus was present in all three subjects.
All three children were treated with neuroendoscopic approach. The ventriculocystostomy was performed in two cases. and ventriculocystocisternostomy in one case. In one case the insertion of cystoperitoneal shunt into the ventriculocystostomy was carried out because of the recurrence of the symptoms.
Results
The abnormal head movements improved after surgery in all three children, with complete resolution of symptoms in two cases. In one case a slight nodding to-and-fro persists on walking.
Conclusions
Neuroendoscopic treatment is a procedure of first choice in symptomatic suprasellar cysts. Both ventriculocystostomy and ventriculocystocisternostomy may lead to the resolution of bobble-head-doll syndrome. According to the literature the bobble-head-doll movement relates to the compression of the dorsomedial nucleus of the thalamus.
The study has been supported by IGA grant ND/7678-3.